Succinylacetone-13C5

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Catalogue number:	PA STI 080290
Chemical name:	Succinylacetone-13C5
CAS Number:	881835-86-5
Category:	miscellaneous compounds,stable isotopes
Synonyms:	4,6-Dioxoheptanoic Acid-13C5; NSC 174804-13C5; 4,6-Dioxoheptanoic-3,4,5,6,7-13C5 Acid; Heptanoic-3,4,5,6,7-13C5 acid, 4,6-dioxo;
Molecular form:	C₂₁₃C₅H₁₀O₄
Appearance:	White Solid
Mol. Weight:	163.12
Storage:	2-8°C Refrigerator
Shipping Conditions:	Ambient
Applications:	Succinylacetone (SA) is a specific marker for the inherited metabolic disease, hepatorenal tyrosinemia. It was developed a stable-isotope for the determination of SA in dried blood spots (DBS) and liquid urine using a 13C4-SA as internal standard.The method was applied retrospectively and prospectively for the diagnosis of hepatorenal tyrosinemia and for follow-up of patients under treatment.